A.I. SAFINA¹, L.M. SALAKHUTDINOVA², A.A. GILMANOV² 

¹Kazan State Medical University, 49 Butlerov St., Kazan, Russian Federation, 420012

²Republican Clinical Hospital of the MH of RT, 138 Orenburgskiy Trakt, Kazan, Russian Federation, 420064

Safina A.I. — intern of the Department of Hospital Therapy with a course of Endocrinology, tel. +7-917-868-91-97, e-mail: aisylu.safina1@mail.ru

Salakhutdinova L.M. — first category cardiologist, tel. (843) 231-21-03, e-mail: salaxluiza@gmail.com

Gilmanov A.A. — first category cardiologist, Head of the Cardiology Department, tel. (843) 231-21-03, e-mail: bip1@rambler.ru

Left ventricular non-compaction (LVNC) is a rare genetic disease of the heart muscle. Making the correct diagnosis of LVNC is important because of the possible complications which are heart failure, ventricular arrhythmias and embolic events and the need for long-term management and screening of living relatives. We also describe a 56-year-old male patient with left ventricular noncompaction (LVNC) who was diagnosed with acute myocardial infarction (MI) and pulmonary embolism. There were provided a series of diagnostic methods for the verification of the syndrome.

Key words: left ventricular non-compaction, cardiomyopathy, heart failure, non coronary-associated ventricular arrhythmias, myocardial infarction.

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