Surgical treatment of neovaginal prolapse in a patient with Mayer — Rokitansky — Kuster — Hauser syndrome (clinical case)
E.R. MEKHTIEVA, A.G. YASHCHUK, I.I. MUSIN, E.M. POPOVA, A.G. IMELBAYEVA, A.A. TYURINA
Bashkir State Medical University of the Ministry of Health of Russia, Ufa
Contact details:
Mekhtieva E.R. — 3rd year postgraduate student of the Department of Obstetrics and Gynecology with the course of IDPO
Address: 3 Lenin St., Russian Federation, Ufa, 450008, tel.: +7-919-606-98-85, e-mail: elvirochka-azn@mail.ru
The article describes a case of complications after surgical treatment of a patient with Mayer — Rokitansky — Kuster — Hauser syndrome, which is characterized by underdevelopment of the Muller ducts derivatives in girls and is manifested by malformations of the vagina and uterus. The features of the diagnosis and surgical treatment of complications using the latest endoscopic techniques are also described.
Key words: Mayer — Rokitansky — Kuster — Hauser syndrome, neovaginal prolapse, promontofixation.
REFERENCES
- Adamyan L.V., Kulakov V.I., Khashukoeva A.Z. Poroki razvitiya matki i vlagalishcha [Malformations of the uterus and vagina]. Moscow: Meditsina, 1998. 327 p.
- Uvarova E.V. Detskaya i podrostkovaya ginekologiya: rukovodstvo dlya vrachey [Pediatric and adolescent gynecology: a guide for physicians]. Moscow: Litterra, 2009. 377 p.
- Kira E.F., Politova A.K., Vyaz’mina K.Yu. Surgical treatment of aplasia of the vagina and cervix using robotics. Vestnik Natsional’nogo mediko-khirurgicheskogo tsentra im. N.I. Pirogova, 2010, vol. 5, no. 2, pp. 130–132 (in Russ.).
- Acien P., Acien M., Sanchez-Ferrer M. Complex malformations of the female genital tract: new types and revision of classification. Hum Reprod, 2004, vol. 19 (10), pp. 2377–2384.
- Herlin M. K., Le V.Q., Hojland A.T., Ernst A., Okkels H., Petersen A.C. et al Whole-exome sequencing identifies a GREB1L variant in a three-generation family with Mullerian and renal agenesis: a novel candidate gene in Mayer — Rokitansky — Kuster — Hauser (MRKH) syndrome. Acasereport. Hum Reprod, 2019, vol. 34, pp. 1838–1846.
- Mamatkulova M.D., Negmadzhanov B.B. Surgical treatment of neovaginal prolapse after sigmoidal colpopoiesis. Problemy sovremennoy nauki i obrazovaniya, 2022, no. 2 (171), pp. 48–52 (in Russ.).
- Musin I.I., Imel’baeva A.G., Mekhtieva E.R. Surgical treatment and prevention of genital prolapse in different age groups. Kreativnaya khirurgiya i onkologiya, 2017, vol. 7, no. 4, pp. 38–42 (in Russ.).
- Musin I.I., Yashchuk A.G., Zaynullina R.M., Naftulovich R.A., Popova E.M., Imel’baeva A.G., Mekhtieva E.R. The principle of choosing surgical technologies in the correction of genital prolapse in different age groups. Prakticheskaya meditsina, 2017, no. 7 (108), pp. 111–114 (in Russ.).