E.Z. FATYKHOVA¹, V.N. MUKHAMADIEVA², A.F. RAKHIMOVA², S.P. YAKUPOVA², T.B. SIBGATULLIN³, M.YU. BADEEVA⁴, M.A. KUNST⁴

 ¹«Vashe zdorovye» Scientific-Research Medical Center, Kazan

²Kazan State Medical University, Kazan

³Kazan State University, Kazan

⁴Republic Clinical Hospital of the Ministry of Healthcare of the Republic of Tatarstan, Kazan

 Contact details:

Fatykhova E.Z. — rheumatologist

Address: 52 Dostoevsky St., Kazan, Russian Federation, 420097, tel.: +7 (843)537-93-93, e-mail: elzafatykhova@mail.ru

Subcutaneous panniculitis-like T-cell lymphoma (SPTCL) is a rare malignant tumor consisting of mature cellulotoxic α—β Т-lymphocytes, which primarily affects subcutaneous adipose tissue. Its clinical and morphological manifestations resemble panniculitis. The incidence of SPTCL is less than 1% of the non-Hodgkin lymphomas. Although the disease debuts at a median age of 35 years, it is found in all age groups. The article presents a clinical case of panniculitis-like T-cell lymphoma in a patient initially diagnosed with recurrent Weber-Christian panniculitis. However, the insufficiently effective therapy led to re-examination of the diagnosis. The timely involvement of doctors of various specialties from the federal center and the high-quality morphological diagnostics made it possible to rapidly make the correct diagnosis and start chemotherapy.

Key words: subcutaneous panniculitis-like T-cell lymphoma, lymphoproliferative diseases, non-Hodgkin lymphomas, skin and subcutaneous adipose tissue lymphoma, panniculitis.

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