N.G. SHAMSUTDINOVA¹, G.I. NURULLINA¹, В.Z. ABDRAKIPOV², Е.V. SUKHORUKOVA², E.V. DYAKOVA², D.R. SADYKOVA¹

¹Kazan State Medical University, Kazan

²Republican Clinical Hospital of the MH of RT, Kazan

 Contact:

Shamsutdinova N.G. ― PhD (medicine), Assistant of the Department of Hospital Therapy

Address: 49 Butlerov Str., Kazan, Russian Federation, 420012, tel. +7-904-763-83-72, e-mail: nailya@e-diva.ru

 Systemic vasculitis is a group of diseases that require rapid diagnosis and timely treatment. Among the clinical diversity of systemic vasculitis forms, a special place is occupied by vasculitis associated with antineutrophilic cytoplasmic antibodies, which have 3 main clinical and pathological variants. The article presents modern data on the clinical picture, diagnosis, and key principles for the management of patients with ANCA-associated vasculitis. A clinical case of severe granulomatosis with polyangiitis is presented.

Key words: systemic vasculitis, granulomatosis with polyangiitis, ANCA-associated vasculitis.

 (For citation: Shamsutdinova N.G., Nurullina G.I., Abdrakipov В.Z., Sukhorukova Е.V., Dyakova E.V., Sadykova D.R. Management of a patient with ANCA-associated vasculitis (clinical case). Practical medicine. 2019. Vol. 17, № 6 (part 1), P. 91-93)

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