E.S. BOBYLEVA¹, A.Yu. GORBUNOV¹, E.V. SUVOROVA², O.I. STARODUBTSEVA³

¹Izhevsk State Medical Academy, 281 Kommunarov Str., 426034 Izhevsk, Russian Federation

²City Clinical Hospital No. 8, 65 Serov Str., 426035 Izhevsk, Russian Federation

³First Republican Clinical Hospital, 57 Votkinskoye shosse, 426000 Izhevsk, Russian Federation

Bobylevа E.S. — post-graduate student of Propedeutics of Internal Diseases with a course of nursing, tel. +7-912-762-36-29, e-mail: lena.bobyleva2017@yandex.ru

Gorbunov A.Yu. — D. Med. Sc., Associate Professor of the Department of Propedeutics of Internal Diseases, tel. 45-20-72, e-mail: gor-a1976@yandex.ru

Suvorova E.V. — doctor-pulmonologist of the highest category of the 2^nd Therapy Department, tel. 45-20-72, e-mail: suvorova-ev@mail.ru

Starodubtseva O.I. — Cand. Med. Sc., doctor-pulmonologist of the highest category, Head of the Pulmonary Department, tel. 46-55-80, e-mail: staroduboksan@mail.ru

Lungs lymphangioleiomyomatosis (LAM) is a rare disease characterized by tumor-like expanding of smooth muscle fibers in the interstitial tissue of lungs, around blood and lymphatic vessels, bronchial tubes, bronchioles, and in lymph nodes, with subsequent cystic transformation of the pulmonary parenchymicatous tissue. The article presents an brief review of literature, as well as a medical case of LAM in young woman with long-term obstructive syndrome.

Key words: medical case, lymphangioleiomyomatosis, obstructive bronchitis, pneumothorax

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