pm mfvt1
    • Main page
      • About journal
      • Articles. Working with contents
      • Editor-in-chief
      • Editorial Council
      • Editorial Board


      • For authors
      • Standards for formatting information
      • Reviewing
      • Politics editorial board
      • Ethics of journal publications


      • For advertisers
      • Subscription
      • About the Publishing House
      • Contact us
  • Hepatolienal syndrome in the practice of a pediatrician

    Редактор | 2017, Lectures for doctors, Practical medicine 10 (17) Pediatrics | 1 декабря, 2017

    M.N. KANKASOVA, O.G. MOKHOVA, O.S. POZDEEVA

    Izhevsk State Medical Academy, 281 Kommunarov Str., Izhevsk, Russian Federation, 426034

     Kankasova M.N. ― Cand. Med. Sc., Associate Professor of the Department of Children’s Infections, e-mail: kankasva@rambler.ru

     The article presents the main causes for hepatolienal syndrome in children and clinical-laboratory features in various diseases. It is highlighted that the maximal prevalence of HLS is observed in children younger than 3 y.o., and its nosoogical structure is different depending on the child’s age. The algorithm of HLS diagnostics is described. The role of comprehensive evaluation of anamnesis is stressed, as well as the clinical data of all organs and systems analysis, and the significance of using a relevant complex of laboratory research methods.

    Key words: hepatolienal syndrome, children, clinics, diagnostics.

    REFERENCES

    1. Surkov A.I. Differential diagnosis of hepatolenal syndrome in children. Praktika pediatra. Gastroenterologiya, 2013, September, pp. 7-15 (in Russ.).
    2. Detskie bolezni. Uchebnik, pod red. N.N. Volodina, Yu.G. Mukhinoy, tom 2 [Children’s diseases. Textbook. Ed. by N.N. Volodina, Yu.G. Mukhina, volume 2]. Gastroenterologiya. Moscow: Dinastiya, 2011. 312 p.
    3. Luchsheva E.V. Osnovnye prichiny gepatolienal’nogo sindroma u detey Kuzbassa, printsipy differentsial’noy diagnostiki: avtoref. dis. … kand. med. nauk [The main causes of hepatolyenal syndrome in children of Kuzbass, the principles of differential diagnosis. Synopsis of dis. PhD med. sciences]. Moscow, 2009. 24 p.
    4. Infektsionnye bolezni: sindromal’naya diagnostika, pod red. N.D. Yushchuka, E.A. Klimovoy [Infectious diseases: syndromic diagnosis. Ed. by N.D. Yuschuk, E.A. Klimova]. Moscow: GEOTAR-Media, 2017. 176 p.
    5. Uchaykin V.F., Cherednichenko T.V., Smirnov A.V. Infektsionnaya gepatologiya. Rukovodstvo dlya vrachey [Infectious hepatology. A guide for doctors]. Moscow: GEOTAR-Media, 2012. 640 p.
    6. Uchaykin V.F., Smirnov A.V., Chuelov S.B. et al. Herpesviral hepatitis in children. Pediatriya, 2012, vol. 91, no. 3, pp. 136-142 (in Russ.).
    7. Moskovskaya I.A. Bolezni pecheni u detey, pod red. M.Ya. Studenikina [Diseases of the liver in children. Ed. by M.Ya. Studenikin]. Tula: Grif i K, 2007. 536 p.
    8. Surkov A.N. Glycogen disease of children. Farmateka dlya praktikuyushchikh vrachey. Pediatriya, 2014, no. 11, pp. 3-15 (in Russ.).
    9. Burda P., Hochuli M. Hepatik glycogen storage disorders:whothave we leaned in recent years ? Curr. Opin. Clin. Nutr. Metab. Care, 2015, 18 (4), pp. 415-421.
    10. Eremina E.Yu. Hemochromatosis. Prakticheskaya meditsina. Pediatriya, 2015, no. 7 (92), pp. 40-44 (in Russ.).
    11. Asanov A.Yu., Sokolov A.A., Volgina S.A. et al. Federal’nye klinicheskie rekomendatsii po diagnostike i lecheniyu bolezni Vil’sona ― Konovalova (gepatolentikulyarnoy degeneratsii) [Federal clinical recommendations for the diagnosis and treatment of Wilson-Konovalov’s disease (hepatolenticular degeneration)]. Saint Petersburg: Litografiya, 2015. 60 p.
    12. EASL. Clinical Practice Gnidehnes: Wilson,s disease. Journal of Hepatology, 2012. vol. 56, pp. 671-685.
    13. Novikov P.V. Lysosomal diseases of accumulation — an urgent problem of pediatrics and modern possibilities of pathogenetic treatment. Rossiyskiy vestnik perinatalogii i pediatrii, 2014, no. 4, pp. 4-9 (in Russ.).
    14. Mikhaylova S.V., Skorobogatova E.,V., Balashov D.V. Federal’nye klinicheskie rekomendatsii po lecheniyu mukopolisakharidoza I tipa (sindrom Gurlera) [Federal clinical guidelines for the treatment of type I mucopolysaccharidosis (Hurler’s syndrome)], 2013. 27 p.
    15. Mc Kay Bounford. P. Hissen. Geneticans Laboratory diagnoctic approach in Niemann Pick disease type C. Journal Neural, 2014, suppl 2, pp. 569-575.
    16. Klyushnikov S.A., Mikhaylov S.V., Dyagtereva A.V. et al. Clinical recommendations for diagnosis and treatment of Niman-Peak type. Meditsinskaya genetika, 2015, vol. 14, pp. 37-51 (in Russ.).
    17. Kaplan P., Baris H., Meileir L. et al. Revised recommendation for the management of Gaucher disease in children. Eur. Journal Pediatr, 2013, Apr, 172 (4), pp. 47-58.
    18. Gundobina O.S., Savost’yanov K.V., Pushkov A.A. Federal’nye klinicheskie rekomendatsii po okazaniyu meditsinskoy pomoshchi detyam s bolezn’yu Goshe [Federal clinical guidelines for the provision of medical care for children with Gaucher disease], 2015. 23 p.
    19. Rumyantsev A.G., Maschan A.A. Federal’nye klinicheskie rekomendatsii po diagnostike i lecheniyu limfomy Khodzhkina (limfogranulematoz) [Federal clinical guidelines for the diagnosis and treatment of Hodgkin’s lymphoma (lymphogranulomatosis)], 2014. 30 p.
    20. Engert A., Eichenauer D.A., Dreyling M. ESMO guidelines working group. Hodgkin’s lymphoma: ESMO clinical recommendations for diagnosis, treatment and follow-up. Ann. Oncol, 2010, 21, pp. 168-71.
    21. Kokolina V.F. et al. Prakticheskoe rukovodstvo po detskim boleznyam: gematologiya detskogo vozrasta [Practical guidance on childhood diseases: childhood hematology]. Moscow: Medpraktika, 2004. Vol. IV. 791 p.
    22. Kaspers G.J, Zimmermann M., Reinhardt D. et al. Improved outcome in pediatric relapsedacute myeloid leukemia: results of a randomized trial on liposomal daunorubicin by the Iternational BFM Study Group. J. Clin. Oncol, 2013, Feb. 10, 31 (5), pp. 599-607.
    23. Rumyantsev A.G., Maschan A.A. Federal’nye klinicheskie rekomendatsii po diagnostike i lecheniyu nasledstvennogo sferotsitoza [Federal clinical guidelines for the diagnosis and treatment of hereditary spherocytosis], 2014. 16 p.
    24. King J., Zanella A. Hereditary red cell membrane and laboratory testing. J. Lab. Hematol, 2013, vol. 35, no. 3, pp. 237-243.

    Метки: 2017, Children, clinics, diagnostics, hepatolienal syndrome, M.N. KANKASOVA, O.G. MOKHOVA, O.S. POZDEEVA, Practical medicine 10 (17) Pediatrics

    ‹ Neuroiinfections in children under present-day conditions Inflammatory and non-inflammatory causes of fever of unknown origin in children ›
    • rus Версия на русском языке


      usa English version site


      Find loupe

      

    • PARTNERS

      пов  logonew
    «Для
    Practical medicine. Scientific and practical reviewed medical journal
    All rights reserved ©