A.A. EVSTRATOV, A.E. CHEREMISIN, R.R. ABBAZOV, D.R. SABIROVA

Republican Clinical Hospital of the MH of RT, Kazan

 Contact details:

Evstratov A.A. ― Head of Resuscitation and Intensive Care Unit №2

Address: 138 Orenburgskiy Trakt, Kazan, Russian Federation, 420064, tel. +7-987-296-22-24, e-mail: virineia2005@mail.ru 

The article presents a literature review and clinical cases of pregnant patients with cystic fibrosis. Cystic fibrosis is a systemic disease, affecting respiratory tract, gastrointestinal tract, liver, pancreas, salivary and sudoral glands, and reproductive system. Respiratory tract pathology is the main cause of complications and lethality (over 90% of cases). The primary manifestations of the disease in adults include respiratory failure in the form of chronic infections and inflammation, weight loss due to malabsorption and pancreatic insufficiency. In women with cystic fibrosis, maternal mortality rate is higher compared with patients without cystic fibrosis. They also have higher levels of intubation ventilation, transfusion of blood components, acute respiratory failure and acute renal failure.

Key words: cystic fibrosis, pregnancy, technique and terms of delivery. 

(For citation: Evstratov A.A., Cheremisin A.E., Abbazov R.R., Sabirova D.R.  Cystic fibrosis as a multisided problem. Literature review and clinical examples. Practical medicine. 2019. Vol. 17, № 6 (part 1), P. 11-14)

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