T.P. MAKAROVA, N.V. AKHMEDGARAEVA, A.V. ISHBULDINA, YU.S. MELNIKOVA, D.A. VDOVIN
Kazan State Medical University
Children’s Republican Clinical Hospital

Makarova Tamara Petrovna
Doctor of Medical Science, Professor of the Department of Hospital Pediatrics
49 Butlerova Str., Kazan 420012
tel. (843) 237-30-37, e-mail: makarova-kgmu@mail.ru 

The clinical case of a patient with polycystic kidney disease with autosomal-recessive mode of inheritance is described. Characteristic and development of clinical and laboratory-instrumental presentation of disease for this patient with an outcome in chronic kidney disease is given. Methods of treatment of patient are described.

Key words: polycystic kidney disease, autosomal-recessive mode of inheritance, chronic kidney disease.

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