Clinical case of monomyelic form of melorheostosis (Leri — Joanny disease)
O.V. TEPLOV1, M.A. CHEKUNOV1, D.KH. GALIMOV1, A.N. NURIAKHMETOV1, R.Z. SALIKHOV1, 2
1Republic Clinical Hospital, Kazan
2Kazan State Medical Academy — Branch Campus of the FSBEI FPE RMACPE MOH Russia, Kazan
Contact details:
Teplov O.V. — junior researcher of the Research Department, traumatologist-orthopedist
Address: 138 Orenburgskiy trakt, Kazan, Russian Federation, 420064, tel.: +7-905-038-30-30, e-mail: Leginaka911@gmail.com
The article presents a clinical case of melorheostosis with lesion of the left lower limb in a 30-year-old woman, involving the hip, knee joints, and foot lesion. Arthrotomy with removal of osteophytes in the posterior part of the knee joint and removal of osteophytes of the foot were performed. In the postoperative period, peroneal nerve neuropathy developed, which required neurolysis and a course of conservative treatment; the neuritis resolved. Later, total hip arthroplasty of the left hip joint was performed and the function of the limb was restored. New surgical interventions may be required in the future.
Key words: melorheostosis, Leri — Joanny disease, total hip arthroplasty, knee arthrotomy.
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