D.R. SABIROVA^1,2, A.R. SHAKIROVA², R.Ya. YAFYASOV², D.Yu. PETRUSHENKO², R.I. GARAEV², R.N. GERASIMOV¹

¹Kazan State Medical University of the Ministry of Health of the Russian Federation, Kazan

²Children’s Republican Clinical Hospital of the Ministry of Health of Republic of Tatarstan, Kazan

Contact:

Sabirova D.R. — PhD (medicine), Associate Professor of the Department of Hospital Pediatrics

Address: 140 Orenburgskiy trakt, 420059, Kazan, Russian Federation, tel. (843) 269-67-69, e-mail: dinasabirova@mail.ru

Inferior vena cava syndrome is a rarely detectable pathology that can proceed both asymptomically and with extensive and debilitating clinical manifestations for patients. The disease is often caused by thrombosis of the inferior vena cava system or its obstruction of various origins. A special case of external compression of the inferior vena cava is the secondary Budd – Chiari syndrome. The article presents a description of the case of inferior vena cava syndrome in a child with ascites. Ascites is most often associated with such diseases as liver cirrhosis, infectious and oncological diseases, heart failure, which required differential diagnosis of ascites. Clinical manifestations were assessed with abdominal ultrasound and RCT. The diagnosis of inferior vena cava syndrome was confirmed with the inferior vena cava phlebography with invasive tensiometry. The child underwent an operation – thoracotomy with the inferior vena cava phlebolysis. After the successful operative treatment, the patient had positive dynamics; clinical manifestations of ascites regressed.

Key words: children, inferior vena cava syndrome, Budd-Chiari syndrome, obstruction, ascites.

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