R.I. DAVLETSHINA¹, G.S. AKHMADULLINA¹, E.G. MENDELEVICH², E.I. BOGDANOV^{1, 2}

¹ Republic Clinical Hospital, Kazan, Russian Federation

² Kazan State Medical University, Kazan, Russian Federation

  Contact details:

Davletshina R.I. – Ph. D. (medicine), neurologist

Address: 138 Orenburgskiy trakt, Kazan, Russian Federation, 420064, tel.: +7 (843) 231-21-02, e-mail: rez-davletshina@yandex.ru

Purpose. To present a unique case of Chiari 1 malformation (MK 1) and hydrocephalus during pregnancy and ways of its operative treatment.

Material and methods. Clinical-neurotic examination of the patient with estimation of foramen magnum symptoms, spinal symptoms, and MRT of postcranial fossa with estimation of tonsils and spinal cord ectopy (tomography MAGNETOM Symphony – 1,5T). Applying the method of operative treatment of endoscopic triventricular cysternostomy.

Conclusion. Chiari 1 malformation (MK 1) is one of the common anomalies with caudal displacement of the cerebellum tonsils. In 30–70% MK 1 is combined with syringomyelia. Much less often, MK 1 can be combined with hydrocephalus, having both a general mechanism of congenital nature, and rare cases of secondary MK 1 development during hydrocephalus formation. We present a clinical case of MK 1 with progressive hydrocephalus and formation of pre-syringomyelia in a young woman in the postpartum period, which was successfully resolved with endoscopic of triventriculostomy. There is a possibility of various cause-effect relations between MK 1 and hydrocephalus. In the described case, the probable mechanism of the development of light compensated MK 1 is hydrocephalus.

Key words: Chiari 1 malformation, hydrocephalus, syringomyelia, foramen magnum, endoscopic triventriculostomy.

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