B.A. AZIZOV

Republican specialized scientific and practical medical Center of endocrinology of the Ministry of Health of the Republic of Uzbekistan, 56 Mirzo Ulugbek St., Tashkent, the Republic of Uzbekistan, 100125

Azizov B.A. — junior research associate of the laboratory of endocrine surgery, tel. (99871) 2622557, e-mail: endocrin@uzsci.net; bakhti78@mail.ru

The problem of multiple endocrine neoplasia is still under study and practitioners know little about it. In the described case the unclassical manifestation of the syndrome MEN-I during 10 years manifested by a combination of nodular hyperplasia of the parathyroid glands, functionally active benign pancreatic tumor and bilateral adrenal hyperplasia. Due to distal pancreatectomy concerning insulinoma the patient had a developed pancreatogenic diabetes with relative insulin deficiency.

Key words: Wermer’s syndrome, MEN-I, hyperparathyroid disorder, insulinoma, hyperinsulinism.

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