G.E. SUKHAREVA

Medical Academy named after S.I. Georgievsky of Vernadsky Crimean Federal University, 5/7 Lenin Av., Simferopol, Republic of Crimea, Russian Federation, 295006

Sukhareva G.E. ― D. Med. Sc., Professor of the Department of Pediatrics with the course of Pediatric Infectious Diseases, tel.: +7-978-762-32-10, e-mail: suchareva@mail.ru

 The article presents the author’s own observations over 16 newborns with atrioventricular block of various degrees. Three patients were diagnosed with Frederick syndrome, which had developed on the 2nd-3rd day of life. Two children with congenital heart defect developed into complete congenital block. The article also describes a rare case of a family form of congenital complete atrioventricular block in two newborns from the same family. The observations illustrate the need for timely prenatal diagnosis of this condition to make a decision about appropriate management of pregnancy and labour in a specialized clinic because of unfavourable prognosis for infants, to exclude concomitant cardiac organic disease of the fetus and to examine the mother and the child simultaneously in order to diagnose latent course of SLE in the mother and cardiac forms of neonatal lupus syndrome in the newborn.

Key words: newborn, atrioventricular block, Frederick syndrome.

REFERENCES

1. Bokeriya E.L. Narusheniya ritma serdtsa u detey pervykh let zhizni [Heart rhythm disturbances in children of the first years of life]. Serdechno-sosudistye zabolevaniya. Sovremennye problemy diagnostiki i lecheniya aritmiy. Izd-vo NTsSSKh im. A.N.Bakuleva RAMN, 2001. Vol. 2, no. 2. Pp. 61-77.
2. Diagnostika i lechenie narusheniy ritma i provodimosti serdtsa u detey: ucheb. Posobie, pod red. M.A. Shkol’nikovoy, D.F. Egorova [Diagnosis and treatment of rhythm disturbances and conduction of the heart in children: Textbook. Ed. by M.A. Shkolnikova, D.F. Egorov]. Chelovek, 2012. Pp. 56-70.
3. Kotlukova N.P., Khuzina O.M., Nemirovskiy V.B., Matyunina E.A. Fetal and neonatal disorders of cardiac rhythm and conduction. Pediatriya, 2007, no. 2 (vol. 86), pp. 6-12 (in Russ.).
4. Sukhareva G.E., Savchuk O.M., Belalova L.Ya. Complete atrioventricular block in children. Tavricheskiy mediko-biologicheskiy vestnik, 1999, no. 3-4, pp. 61-65 (in Russ.).