V.I. ILINSKIY², N.G. SHAMSUTDINOVA¹, G.I. NURULLINA¹, L.I. MINGAZOVA², V.O. MITRIKOVA¹, A.A. SAYFEEVA¹

¹Kazan State Medical University of the MH of RF, 49 Butlerov Str., Kazan, Russian Federation, 420012

²Republican Clinical Hospital of the Ministry of Healthcare of the Republic of Tatarstan, 138 Orenburgskiy trakt, Kazan, Russian Federation, 420064

 Ilinskiy V.I. ― Head of the Pulmonology Department, tel. (843) 237-36-26, e-mail: Victor.Ilinskiy@tatar.ru

Shamsutdinova N.G. ― D. Sc. (medicine), Assistant of the Department of Hospital Therapy, e-mail: nailya@e-diva.ru

Nurullina G.I. ― Assistant of the Pulmonology Department, e-mail: nurguzel@mail.ru, ORCID ID: 0000-0002-7697-187X

Mingazova L.I. ― Doctor of the Pulmonology Department, tel. (843) 237-36-26, e-mail: Victor.Ilinskiy@tatar.ru

Mitrikova V.O. ― the 4^th year student of the Faculty of Medicine, e-mail: v.mitrikova@mail.ru, ORCID ID:  0000-0002-5392-6144

Saifeeva A.A. ― the 4^th year student of the Faculty of Medicine, e-mail: m172463@mail.ru, ORCID ID:  0000-0002-6335-4733

The article presents information about the disease «alveolar proteinosis», its forms, clinical manifestations and prognosis are considered. The issues of etiology, pathogenesis and diagnosis of pulmonary alveolar proteinosis (PAP) are outlined. To diagnose the described unique clinical case, modern diagnostic methods were applied. After confirming the diagnosis, the patient underwent high-volume therapeutic bronchoalveolar lavage of both lungs. As a result of the treatment, a significant improvement in the patient’s condition was achieved, which indicates the effectiveness of the treatment.

Key words: alveolar proteinosis, clinical forms, prognosis, respiratory failure.

 (For citation: Ilinskiy V.I., Shamsutdinova N.G., Nurullina G.I., Mingazova L.I., Mitrikova V.O., Saifeeva A.A. Alveolar proteinosis as a rare case of in the practice of a pulmonologist. Practical Medicine. 2018)

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