L.V. TITOVA^1,2, S.N. IVANOVA^1,2, S.A. GLADKOV^1,2, YU.B. LOCHOVA²

 ¹Northern State Medical University, Arkhangelsk, Russia

²Arkhangelsk Regional Clinical Hospital, Arkhangelsk, Russia

 Contact details:

Ivanova S.N. — PhD (medicine), Associate Professor of the Department of Hospital Therapy and Endocrinology

Address: 51 Troitsky prospekt, Arkhangelsk, Russian Federation, 163045, tel.: +7 (8182) 285-951, e-mail: sivanova09@mail.ru

The purpose — to present literature data on the peculiarities of diagnosis and the course of a rare intravascular large B-cell lymphoma (ICBCCL), as well as a clinical case.

Material and methods. The article presents a description of the clinical observation of ICBCCL under the guise of a rheumatological disease, verified at autopsy by an immunohistochemical method.

Conclusion. The article is of interest to practitioners, since ICBCCL is a rare form of diffuse large B-cell lymphomas with varied clinical and aggressive course. The key diagnostics for ICBCCL is skin biopsy and immunohistochemical examination.

Key words: systemic lupus erythematosus, idiopathic paraneoplastic dermatomyositis, intravascular large B-cell lymphoma, telangiectasia. 

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