S.L. MOROZOV^1,2,3, O.V. POLYAKOVA², N.V. YANOVSKAYA², A.V. ZVEREVA², V.V. DLIN¹

 ¹Scientific-research Clinical Institute for Pediatrics named after Acad. Yu.E. Veltishchev of the Russian Scientific-research Medical University named after N.I. Pirogov, Moscow

²Russian Scientific-research Medical University named after N.I. Pirogov, Moscow

³Lapino Clinical Hospital of “Mat i Ditya” Group, Moscow region

 Contact:

Morozov S.L. ― PhD (medicine), Senior Researcher of the Department of Inherited and Acquired Kidney Diseases, Associate Professor of the Department of Hospital Pediatrics No. 2 of Pediatrics Faculty

Address: 2 Taldomskaya Str., 125412, Moscow, Russian Federation, tel.: +7-903-138-77-32, e-mail: [email protected]

Spina Bifida is a congenital malformation in which a defect in the spine development occurs as a result of the incorrect closure of the embryonic neural tube. At present, the disease presents a large problem, as in most cases it leads to disability of patients, while the absence of pathogenetic therapy and rehabilitation systems make this problem especially urgent. In the article, modern approaches and opportunities for the diagnosis, treatment and rehabilitation of children with this pathology are discussed. The article also presents data on the first patients operated on in utero in the Russian Federation, as well as modern approaches to the diagnosis, surgical treatment, and rehabilitation of these children.

Key words: Children, Spina Bifida, malformation, intrauterine correction, rehabilitation, perinatal diagnosis.

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