Noncompact myocardium — a difficult path to diagnosis
A.A. MALOV1, R.A. BASHIROV2, A.F. YUSUPOVA1, S.A. ALIMOVA1
1Kazan State Medical University, 49 Butlerov Str., Kazan, Russian Federation, 420012
2Republic Clinical Hospital of the MH of RT, 138 Orenburgskiy Trakt, Kazan, Russian Federation, 420064
Malov A.A. — Assistant of the Department of Hospital Therapy, tel. +7-950-323-56-85, e-mail: [email protected]
Bashirov R.A. — doctor of the Radiology Department, tel. +7-917-396-15-94, e-mail: [email protected]
Yusupova A.F. — Cand. Med. Sc., Associate Professor of the Department of Oncology, Radiation Diagnostics and Radiotherapy tel. +7-987-290-64-27, e-mail: [email protected]
Alimova S.A. — student of the Therapy and Prevention Faculty, tel. +7-987-214-36-05, e-mail: [email protected]
Noncompact myocardium is a form of cardiomyopathy, which characteristic feature is a pathological hyper-trabecular of the left ventricle myocardium, with a normal and noncompact myocardium layers. The pathogenesis and clinical manifestation are composed of the leading syndromes: heart failure, arrhythmias, and thromboembolic syndrome. Taking into account the non-specific character of these manifestations, unfavorable prognosis and high lethality, the instrumental methods play the major role in diagnosing this disease. The article describes approaches to multi-modal radial semiotics and differential diagnostics of noncompact myocardium. The diagnostic algorithm includes the role of single-photon emission computer tomography (SPECT) of myocardium with Tc99m «Technetril», magnetic-resonance tomography (MRT) of heart with contrasting paramagnetic medications based on gadolinium.
Key words: cardiomyopathy, noncompact myocardium, single-photon emission computer tomography (SPECT) of myocardium, magnetic resonance tomography (MRI) of heart.
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