A.A. MALOV¹, R.A. BASHIROV², A.F. YUSUPOVA¹, S.A. ALIMOVA¹

¹Kazan State Medical University, 49 Butlerov Str., Kazan, Russian Federation, 420012

²Republic Clinical Hospital of the MH of RT, 138 Orenburgskiy Trakt, Kazan, Russian Federation, 420064

 Malov A.A. — Assistant of the Department of Hospital Therapy, tel. +7-950-323-56-85, e-mail: [email protected]

Bashirov R.A. — doctor of the Radiology Department, tel. +7-917-396-15-94, e-mail: [email protected]

Yusupova A.F. — Cand. Med. Sc., Associate Professor of the Department of Oncology, Radiation Diagnostics and Radiotherapy tel. +7-987-290-64-27, e-mail: [email protected]

Alimova S.A. — student of the Therapy and Prevention Faculty, tel. +7-987-214-36-05, e-mail: [email protected]

Noncompact myocardium is a form of cardiomyopathy, which characteristic feature is a pathological hyper-trabecular of the left ventricle myocardium, with a normal and noncompact myocardium layers. The pathogenesis and clinical manifestation are composed of the leading syndromes: heart failure, arrhythmias, and thromboembolic syndrome. Taking into account the non-specific character of these manifestations, unfavorable prognosis and high lethality, the instrumental methods play the major role in diagnosing this disease. The article describes approaches to multi-modal radial semiotics and differential diagnostics of noncompact myocardium. The diagnostic algorithm includes the role of single-photon emission computer tomography (SPECT) of myocardium with Tc99^m «Technetril», magnetic-resonance tomography (MRT) of heart with contrasting paramagnetic medications based on gadolinium.

Key words: cardiomyopathy, noncompact myocardium, single-photon emission computer tomography (SPECT) of myocardium, magnetic resonance tomography (MRI) of heart.

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