Diagnosis of Weber — Christian panniculitis
S.F. AKHMEROV¹, D.I. ABDULGANIYEVA¹, S.A. LAPSHINA¹, R.Z. ABDRAKIPOV², M.A. AFANASYEVA², E.V. SUKHORUKOVA², R.A. DZAMUKOV², G.A. KHABIBULLINA¹, E.R. KHOSNETDINOVA¹
1Kazan State Medical University, 49 Butlerov St., Kazan, Russian Federation, 420012
2Republican Clinical Hospital of the Ministry of Healthcare of the Republic of Tatarstan, 138 Orenburgskiy Trakt, Kazan, Russian Federation, 420064
Akhmerov S.F. — Cand. Med. Sc., Associate Professor of the Department of Hospital Therapy, tel. +7-909-308-33-37, e-mail: [email protected]1
Abdulganieva D.I. — D. Med. Sc., Associate Professor, Head of the Department of Hospital Therapy, tel. +7-987-296-27-68, e-mail: [email protected]1
Lapshina S.A. — Cand. Med. Sc., Assistant Lecturer of Hospital Therapy Department, tel. +7-987-290-15-65, e-mail: [email protected]1
Abdrakipov R.Z. — Head of Rheumatology Department, tel. +7-965-607-97-70, e-mail: [email protected]2
Afanasyeva M.A. — doctor of Rheumatology Department, tel. +7-917-273-12-94, e-mail: [email protected]2
Sukhorukova E.V. — doctor of Rheumatology Department, tel. +7-917-270-85-24, e-mail: [email protected]2
Dzamukov R.A. — Cand. Med. Sc., Head of the Pathology-Anatomy Department with cytological laboratory, tel. +7-917-278-87-34, e-mail: [email protected]2
Khabibullina G.A. — resident doctor of the Department of Hospital Therapy, tel. +7-927-405-71-27, e-mail: [email protected]1
Khosnetdinova E.R. — resident doctor of Hospital Therapy Department, tel. +7-927-469-96-47, e-mail: [email protected]1
The article presents the literature data and clinical observation of a patient with Weber — Christian disease. The authors demonstrate the complexity of the diagnostic search in this nosology. The correct and timely diagnosis and treatment determine a good prognosis in patients with Weber — Christian panniculitis.
Key words: Weber — Christian disease, panniculitis, nodular of Pfeifer — Weber — Christian panniculitis, idiopathic immunoallergical adipose tissue inflammation, lipogranuloma.
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