S.F. AKHMEROV¹, D.I. ABDULGANIYEVA¹, S.A. LAPSHINA¹, R.Z. ABDRAKIPOV², M.A. AFANASYEVA², E.V. SUKHORUKOVA², R.A. DZAMUKOV², G.A. KHABIBULLINA¹, E.R. KHOSNETDINOVA¹ 

¹Kazan State Medical University, 49 Butlerov St., Kazan, Russian Federation, 420012

²Republican Clinical Hospital of the Ministry of Healthcare of the Republic of Tatarstan, 138 Orenburgskiy Trakt, Kazan, Russian Federation, 420064

Akhmerov S.F. — Cand. Med. Sc., Associate Professor of the Department of Hospital Therapy, tel. +7-909-308-33-37, e-mail: [email protected]¹

Abdulganieva D.I. — D. Med. Sc., Associate Professor, Head of the Department of Hospital Therapy, tel. +7-987-296-27-68, e-mail: [email protected]¹

Lapshina S.A. — Cand. Med. Sc., Assistant Lecturer of Hospital Therapy Department, tel. +7-987-290-15-65, e-mail: [email protected]¹

Abdrakipov R.Z. — Head of Rheumatology Department, tel. +7-965-607-97-70, e-mail: [email protected]²

Afanasyeva M.A. — doctor of Rheumatology Department, tel. +7-917-273-12-94, e-mail: [email protected]²

Sukhorukova E.V. — doctor of Rheumatology Department, tel. +7-917-270-85-24, e-mail: [email protected]²

Dzamukov R.A. — Cand. Med. Sc., Head of the Pathology-Anatomy Department with cytological laboratory, tel. +7-917-278-87-34, e-mail: [email protected]²

Khabibullina G.A. — resident doctor of the Department of Hospital Therapy, tel. +7-927-405-71-27, e-mail: [email protected]¹

Khosnetdinova E.R. — resident doctor of Hospital Therapy Department, tel. +7-927-469-96-47, e-mail: [email protected]¹ 

The article presents the literature data and clinical observation of a patient with Weber — Christian disease. The authors demonstrate the complexity of the diagnostic search in this nosology. The correct and timely diagnosis and treatment determine a good prognosis in patients with Weber — Christian panniculitis.

Key words: Weber — Christian disease, panniculitis, nodular of Pfeifer — Weber — Christian panniculitis, idiopathic immunoallergical adipose tissue inflammation, lipogranuloma.

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