T.I. KHAYBULLIN^1, 2, F.A. KHABIROV^1,2, L.A.AVERIANOVA^1, 2, G.M. AKHMEDOVA¹, N.N. BABICHEVA², E.V. GRANATOV²

¹ Kazan State Medical Academy, 11 Mushtary St., Kazan, Russian Federation, 420012

² Republican Clinical Diagnostic Center for Demyelinating Diseases of the Ministry of Healthcare of the Republic of Tatarstan, 13 Vatutina St., Kazan, Russian Federation, 420021

Khaybullin T.I. — PhD (Medicine), Associate Professor of the Department of Neurology and Manual Therapy, tel. (843) 278-88-29, e-mail: [email protected]^1,2

Khabirov F.A. — D. Med. Sc., Professor, Head of the Department of Neurology and Manual Therapy, tel. (843) 278-97-28, e-mail: [email protected]

Averianova L.A. — neurologist, tel. (843) 278-88-29, e-mail: [email protected]^1,2

Akhmedova G.M. — PhD (Medicine), Associate Professor of the Department of Neurology and Manual Therapy, tel. (843) 278-88-29, e-mail: [email protected]¹

Babicheva N.N. — neurologist, tel. (843) 278-88-29, e-mail: [email protected]²

Granatov E.V. — PhD (Medicine), neurologist, tel. (843) 278-88-29, e-mail: [email protected]²

Current information about chronic inflammatory demyelinating polyradiculoneuropathy (CIDP) and related syndromes is presented. The etiology and pathogenesis of the disease are discussed, as well as the typical and atypical clinical picture of CIDP, with the characteristics of each form of polyneuropathy. Diagnostic criteria of CIDP, allowing to confirm or exclude this disease, are presented. Principles of CIDP treatment by anti-inflammatory and immunomodulatory drugs are considered in the final part of the article.

Key words: chronic inflammatory demyelinating polyradiculoneuropathy, multifocal motor neuropathy, multifocal sensory and motor neuropathy, distal symmetric chronic demyelinating neuropathy, chronic inflammatory polyradiculoneuropathy, chronic acquired demyelinating polyneuropathy.

 

 

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